[HTML][HTML] Glomerulonephritis with isolated C3 deposits as a manifestation of subtotal factor I deficiency

I Boudhabhay, V Frémeaux-Bacchi… - Kidney International …, 2019 - Elsevier
… Deficiency of FI is a very rare primary immunodeficiency, inherited as an … both pathological
entities, which share common molecular mechanisms … Haemolytic uraemic syndrome

[HTML][HTML] Complement dysregulation in glomerulonephritis

K Kaartinen, A Safa, S Kotha, G Ratti, S Meri - Seminars in immunology, 2019 - Elsevier
… of primary GN (like IgA glomerulonephritis, dense deposit disease, C3 glomerulonephritis,
post… that lead to the development of C3GN or to atypical haemolytic uremic syndrome (aHUS). …

Update on C3 glomerulopathy: a complement-mediated disease

F Caravaca-Fontán, L Lucientes, T Cavero, M Praga - Nephron, 2020 - karger.com
C3 glomerulopathy (C3G) is a clinicopathologic entity … ), and C3 glomerulonephritis (C3GN),
in which deposits may be … immunofluorescence staining for C3, either isolated or at least two …

C3 glomerulopathy—understanding a rare complement-driven renal disease

RJH Smith, GB Appel, AM Blom, HT Cook… - Nature reviews …, 2019 - nature.com
C3 glomerulopathies are rare diseases that share an … into dense deposit disease (DDD)
and C3 glomerulonephritis (… of allograft failure in 189,211 primary kidney transplant recipients …

C3 glomerulopathy and atypical hemolytic uremic syndrome: an updated review of the literature on alternative complement pathway disorders

K Turkmen, I Baloglu, H Ozer - International Urology and Nephrology, 2021 - Springer
… they could be a continuation of the same entity [3, 4]. Historically, … However, since both
primary and secondary MPGN … , it has been found that isolated C3 deposited idiopathic MPGN-…

[HTML][HTML] Diverse clinical presentations of C3 Dominant glomerulonephritis

RM Hanna, J Hou, H Hasnain, F Arman… - Frontiers in …, 2020 - frontiersin.org
C3 glomerulonephritis (C3GN) and dense deposit disease (… /mL], and there was isolated
depression of C3 at 67 mg/dL [… The importance of both genetic and environmental risk factors

Glomerular Disease of Complement Dysregulation (C3 Glomerulopathy, Atypical Hemolytic-Uremic Syndrome)

M Lemaire, BP Dixon - Handbook of Glomerulonephritis, 2022 - books.google.com
… with atypical hemolytic and uremic syndrome: genetic complement … C3 glomerulonephritis
and dense deposit disease share a … in nephrotic syndrome due to primary glomerulonephritis. …

A clinical approach to children with C3 glomerulopathy

M Vivarelli, N van de Kar, R Labbadia… - Pediatric …, 2022 - Springer
C3 glomerulopathy is a relatively new clinical entity that … pathway activation appears to be
the primary cause of C3G [13] … these C3 glomerulonephritis (C3GN) patients, the C3 deposits

Membranoproliferative glomerulonephritis and C3 glomerulopathy

D Gale, M Owen-Casey - Primer on Nephrology, 2022 - Springer
… and is the underlying primary glomerulopathy in 5–… deposit disease, whereas complement
dysregulation at endothelial surfaces typically leads to atypical haemolytic uraemic syndrome. …

C3 glomerulopathies: dense deposit disease and C3 glomerulonephritis

C Ponticelli, M Calatroni, G Moroni - Frontiers in Medicine, 2023 - frontiersin.org
… renal disorders that share certain common histologic features… of differentiating between these
entities for management and … C3 or C4 are classified as primary GN and are defined as C3